Seckel syndrome with polyarteritis nodosa.

نویسندگان

  • Ramazan Kutlu
  • Alpay Alkan
  • Onur Kutlu
  • Cengiz Yakinci
چکیده

Seckel syndrome is a rare genetic disorder with a typical "bird-headed" appearance. It could affect many organ systems but renal involvement is uncommon. Polyarteritis nodosa is systemic vasculitic disorder which also involves kidneys. We report a case of Seckel syndrome in a 9 year-old boy with renal involvement due to polyarteritis nodosa. According to the literature, this is the first report of polyarteritis nodosa in Seckel syndrome.

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عنوان ژورنال:
  • Indian pediatrics

دوره 41 11  شماره 

صفحات  -

تاریخ انتشار 2004